IngentaConnect Proteus syndrome with widespread portwine stain naevus

Authors: PLÖtz^{1, 2}; Abeck³; Ring³

Source: British Journal of Dermatology, Volume 139, Number 6, December 1998 , pp. 1060-1063(4)

Publisher: Blackwell Publishing

Key:

- Free Content

- New Content

- Subscribed Content

- Free Trial Content

Abstract:

Proteus syndrome is a rare condition comprising asymmetrical overgrowth of different parts of the body in association with various cutaneous abnormalities. We describe a 3-year-old boy with Proteus syndrome, who presented with hemihypertrophy of the right leg, asymmetric macrodactyly, subcutaneous masses and a widespread portwine stain interspersed with angiokeratomas on the right leg, scrotum and on the middle and left side of the back. Doppler ultrasound of the right leg did not show hypercirculation, but did reveal the absence of the right superficial femoral vein.

Document Type: Case report

DOI: 10.1046/j.1365-2133.1998.02566.x

Affiliations: 1: Research Center Borstel, Germany, 2: Department of Orthopedic Surgery, Medical University, Lübeck, Germany 3: Department of Dermatology and Allergy Biederstein, Technical University Munich, Biedersteiner Str. 29, 80802 Munich, Germany,

The full text electronic article is available for purchase. You will be able to download the full text electronic article after payment.

$50.16 plus tax Refund Policy